Gourt > Health > Conditions and Diseases > Rare Disorders > Moyamoya
Moyamoya disease is an extremely rare disorder in most parts of the world except in Japan. The pathogenesis of Moyamoya disease is unknown. Moyamoya disease is characterized by progressive intracranial vascular stenoses of the circle of Willis, resulting in successive ischemic events. Hemmorhagic events can also occur. The condition leads to irreversible blockage of the main blood vessels-the carotid arteries- to the brain as they enter into the skull. It is a disease that tends to affect children and adults in the third to fourth decades of life. In children it tends to cause strokes or seizures. In adults it tends to cause bleeding or strokes. The clinical features are cerebral ischaemia (strokes), recurrent transient ischaemic attacks (TIA's or "mini strokes"), sensorimotor paralysis (numbness in the extremeties), convulsions and/or migraine-like headaches.
The process of blockage (vascular occlusion) once it begins tends to continue despite any known medical management unless treated with surgery. The repeated strokes can lead to severe functional impairment or even death so it is important to recognize these lesions and treat them early on. Without treatment, there is progressive deterioration of neurologic function and re-hemorrhage.
The diagnosis is initially suggested by CT, MRI, or angiogram. Contrast-enhanced T1-weighted images are better than FLAIR images for depicting the leptomeningeal ivy sign in moyamoya disease. MRI and MRA should be performed for the diagnosis and follow-up of moyamoya disease. Diffusion-weighted imaging can also be used for following the clinical course of children with moyamoya disease, in whom new focal deficits are highly suspicious of new infarcts.
More on [ Moya Moya Disease ]
Vascular Disorders
Brain Diseases
RT @John1720 RT @PoppiesBlooming: Please pray for little Polly, having brain surgery now for Moyamoya disease. Pls RT Thank you!
NWGramma (Linda Long) Thu, 17 Dec 2009 21:33:26 -0000
RT @John1720 RT @PoppiesBlooming: Please pray for little Polly, having brain surgery now for Moyamoya disease. Pls RT Thank you!
RT @PoppiesBlooming: Please pray for little Polly, having brain surgery now for Moyamoya disease. Pls RT Thank you!
John1720 (John Treiber) Thu, 17 Dec 2009 21:25:15 -0000
RT @PoppiesBlooming: Please pray for little Polly, having brain surgery now for Moyamoya disease. Pls RT Thank you!
RT @gap79 RT @braewood: RT @PoppiesBlooming: Please pray for little Polly, having brain surgery now for Moyamoya disease. Pls RT Thank you!
Prayer_Network (Prayer Network) Thu, 17 Dec 2009 19:22:31 -0000
RT @gap79 RT @braewood: RT @PoppiesBlooming: Please pray for little Polly, having brain surgery now for Moyamoya disease. Pls RT Thank you!
RT @braewood: RT @PoppiesBlooming: Please pray for little Polly, having brain surgery now for Moyamoya disease. Pls RT Thank you!
gap79 (Glenn Prawito) Thu, 17 Dec 2009 19:18:16 -0000
RT @braewood: RT @PoppiesBlooming: Please pray for little Polly, having brain surgery now for Moyamoya disease. Pls RT Thank you!
RT @braewood RT @PoppiesBlooming: Please pray for little Polly, having brain surgery now for Moyamoya disease. Pls RT Thank you!
Prayer_Network (Prayer Network) Thu, 17 Dec 2009 17:22:40 -0000
RT @braewood RT @PoppiesBlooming: Please pray for little Polly, having brain surgery now for Moyamoya disease. Pls RT Thank you!
RT @PoppiesBlooming: Please pray for little Polly, having brain surgery now for Moyamoya disease. Pls RT Thank you!
braewood (Sandy) Thu, 17 Dec 2009 17:20:29 -0000
RT @PoppiesBlooming: Please pray for little Polly, having brain surgery now for Moyamoya disease. Pls RT Thank you!
Moyamoya Disease - Definition, clinical symptoms and radiographic finding.
Meta Description: [ a CHORUS notecard document about moyamoya disease ]
Moyamoya Disease - Diagnosis, treatment and prognosis, plus problems specific to women.
Meta Description: [ Moyamoya Disease: Medical information on moyamoya disase is provided by a Japanese neurosurgeon. ]
Moyamoya Disease - Support group for those diagnosed with this condition and their families. Includes medical information, personal account, links and a message board.
Meta Description: [ Pictures of my MoyaMoya Disease STA-MCA surgery for MoyaMoya sufferers and their families ]
NINDS: Moyamoya Disease - Description, treatment and prognosis from the National Institute of Neurological Disorders and Stroke.
Meta Description: [ Moyamoya disease information page compiled by the National Institute of Neurological Disorders and Stroke (NINDS). ]
NORD: Moyamoya Disease - Sample report, plus links to organisations. [Fee required for full report]
Meta Description: [ National Organization for Rare Disorders is dedicated to helping people with rare, orphan diseases. Rarediseases.org contains information on the prevention, treatment and cure of rare diseases. ]
Pediatric Oncall - Offers moyamoya disease case reports.
Meta Description: [ Moyamoya Disease Case Reports Pediatric Oncall ]
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